Hereditary spherocytosis is still rare disease in our country, on the other hand, has been found in many population especially in Nothern Europian peoples".
It is transmitted as a Mendelian autosomal dominant and is characterized by the erythrocytes are small, but variable in size, thick and spherical without central pallor, which have increased osmotic fragility in the peripheral blood smear´s).
We have experienced a case of -unfamilial sporadic spherocytosis of eleven year did primary school girl, who has had hemolytic anemia, anemic crisis, splenomegaly, lethargy, intermittent slight jaundice, numular dermatitis, typical´ picture of spherocytosis in peripheral blood smear and moderately increased osmotic fragility of erythrocytes.
We treated with surgically, underwent splenectomy, for this patient. Splenectomy resulted in clinical cure with clearing of jaundice, and improving anemia without any other trouble. Reference were also reviewed:
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